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Saturday, September 4, 1999


07.30 - 08.30 Clinical Conference T3 AUDITORIUM 1
ELECTRONIC COMMUNICATION MEDIA: NEW TOOLS OF THE TRADE IN CLINICAL PROBLEM SOLVING
F. Schaefer (Germany)
J. Vejvalka (Czech Republic)

The remarkable growth of the Internet over the past few years has an enormous impact on everyday medical care. The availability of freely accessible literature and knowledge databases and expert email networks offers new perspectives to clinical problem solving to clinicians in academic, non-academic and private settings alike. For the first time in history, these innovations have paved the way for the global performance of rational, standardized evidence-based medicine. Moreover, medical information has become directly available to patients, who increasingly confront their physicians with 'downloaded' knowledge. Pediatric nephrologists should know how to keep pace with these developments and make best use of the new methodologies. In this clinical conference we will provide up-to-date information on how to utilize medical knowledge libraries and renal expert networks in the internet to obtain help in diagnostic problems as well as in clinical decision-making.


07.30 - 08.30 Clinical Conference T4 AUDITORIUM 2
DIALYSIS IN YOUNG CHILDREN
M. Fischbach (France)
C. Schröder (The Netherlands)

Dialysis in young children may be performed either by hemodialysis or by peritoneal dialysis, but the most commonly used method is peritoneal dialysis. This choice is in agrement with technical facilities, with child development respect ie dialysis and care, both at home by parents direct implication, with continuous dialysis, each day assuring at the best dry weight managment and optimal blood purification. Peritoneal dialysis prescription in children, especially in young children could be enhanced by the better comprehension of the peritoneal membrane capacity often described as "hyperpermeable". This something "false" concept is the result form many successive approximations:
• Firstly, characterisation of the permeability of the peritonium thanks to the peritoneal equilibration test (PET) which is only an appreciation of the ratio of fill volume per fonctionnal peritoneal membrane area available for exchange.
• Secondly prescription of the fill volume scalled for body weight, kg. in place of BSA, m2. The peritoneal membrane area is in the same range through the patients age if scalled for BAS; on the contrary this area is two fold higher in infants compared to adults if expressed per kg. Therefore, the prescription of a fill volume scalled per body weight favours a state of a low ration, fill volume per area for exchange, that is an induced "hyperpermeability" state.
• Thirdly recruitment of the peritoneal area available for exchange both dependent from the fill volume, and from the posture. The area increases with fill volume but seems to peak around a fill volume of 1400 ml/m2 ie Ao/Ax 24000 ą 1450 cm/m2/1.73 m2. Ao/Ax fall significantly when the patients were standing compared to the value obtained in supine position.


08.35 - 09.15 State of the Art Lecture L3 AUDITORIUM 1
NEPHROPATHIC CYSTINOSIS: FROM CLINICAL OBSERVATION TO MOLECULAR ANALYSIS
M. Broyer (France)
Chairperson: C. Chantler (United Kingdom)

9.15 - 9.45 Coffee Break

09.45 - 11.15 Symposium S5 AUDITORIUM 1
RENAL REPLACEMENT THERAPY: QUALITY OF LIFE AND ETHICAL ASPECTS
Chairperson: A. Watson (UK), J. Pekárková (Czech Republic)

Round table participants: U. Berg (Sweden), H. Mocan (Turkey). A. Bensman (France)


9.45 - 11.15 Symposium S6 AUDITORIUM 2
NEW METHODS FOR THE IMAGING OF URINARY TRACT
Chairperson: K. Verrier-Jones (United Kingdom), U. Jodal (Sweden)

• IMAGING OF KIDNEY AND URINARY TRACT BY DMSA AND MAG3: WHEN, WHICH?
  E. Girardin (Switzerland)
• IMAGING OF REFLUX BY ECHO-ENHANCED VOIDING UROSONOGRAPHY
  J. Tröger (Germany)
• MR UROGRAPHY, A FUTURE GOLD STANDARD IN UROLOGICAL IMAGING?
a) Experimental studies - W.M. Rohrschneider (Germany)
b) Clinical studies - A. Borthne (Norway)


11.15 - 11.45 Lunch

11.45 - 13.15 Poster Sessions

Poster Session 1b)
MOLECULAR GENETICS

Chairperson: L. Monnens (The Netherlands), K. Zerres (Germany)

P14 THE MOLECULAR-GENETIC INVESTIGATIONS IN X-LINKED ALPORT´S SYNDROME (X-AS)
F. Tsalicova, S. Tverskaya, V. Fokeeva, O. Turpitko, M. Ignatova (Russia)
P15 COMPOUND DELETION OF THE rhoGAP C1 AND THE ARGININ-VASOPRESSIN-V2 RECEPTOR GENES IN A PATIENT WITH NEPHROGENIC DIABETES INSIPIDUS
T. Schöneberg, K. Pasel, A. Schulz, V. v. Baer, H.-D. Volk, T. Gudermann, G. Filler (Germany)
P17 EVIDENCE FOR NEW GENE LOCI FOR AUTOSOMAL DOMINANT MEDULLARY CYSTIC KIDNEY DISEASE (ADMCKD)
A. Fuchshuber, S. Kroiß, M. Jung, K. Huck, S. Berthold, A. Reis, D. Krieter, T. Feest, C. Burton, A.Gal, G. Ghiggeri, G. Caridi, F. Scolari, F. Hildebrandt (Germany)
P18 GENETIC DIAGNOSIS OF AUTOSOMAL DOMINANT POLYCYSTIC KIDNEY DISEASE IN CHILDREN AT RISK
G. Ariceta, M. Vila, L. Arrojo, M. Otero, G. Pazos, R. Alonso, T. Cordal, S. Dávila, X.M. Lens (Spain)
P19 ACTIVATION BY ANGII OF COL3A1 PROMOTER ACTIVITY WITHIN RENAL CELLS "IN VITRO"
G.M. Ghiggeri, R. Oleggini, S. Menoni, L. Musante, M. Giampuzzi, R. Gusmano, R. Ravazzolo, F. Perfumo (Italy)
P20 MAPPING A NEW LOCUS FOR AUTOSOMAL DOMINANT MEDULLARY CYSTIC KIDNEY DISEASE ON CHROMOSOME 16
G. Caridi, F. Scolari, A. Amoroso, G. Casari, R. Gusmano, F. Perfumo, G.M. Ghiggeri (Italy)
P21 CLONING AND CHARACTERIZATION OF THE PROMOTER REGION OF RAT TAURINE
R.W. Chesney (USA)
P22 MOLECULAR BASIS OF FAMILIAL MEDITERRANEAN FEVER IN TURKEY
N. Akar, M. Misirhoglu, F. Yalcinkaya, N. Cakar, N. Tümer, M. Akcakus, H. Tastan, Y. Matzner (Turkey)
P23 NEPHROCYSTIN, THE PRODUCT OF THE NEPHRONOPHTISIS-1 GENE, IS EXPRESSED
F. Hildebrandt, E. Otto, B. Lescher, C. Rensing, S. Schätzle, A. Kispert (Germany)
P24 BARTTER SYNDROME WITH SENSORINEURAL DEAFNESS: MOLECULAR GENETICS
F. Hildebrandt, F. Beekmann, R. Ruf, H.G. Nothwang, C. Klein, M. Vollmer (Germany)
P25 ALPORT SYNDROME: THE EXPERIENCES IN MOLECULAR DIAGNOSTICS IN THE CZECH REPUBLIC
Š. Krejčová, V. Maoška, P. Hedvičáková, M. Šutajová, J. Stejskal, J. Janda (Czech Republic)

Poster Session 2b)
ACUTE RENAL FAILURE

Chairperson: W. Proesmans (Belgium), L.B. Zimmerhackl (Germany)

P40 PROTECTION WITH N-ACETYL CYSTEINE (NAC) PLUS ?-TOCOPHEROL (?T) AGAINST ACUTE RENAL DAMAGE BY CYCLOSPORINE (CSA). HISTOLOGICAL EVIDENCES.
I. Bravo, C. Bosco, R. Rodrigo, M. Orellana, L. Thielemann (Chile)
P41 THE ROLE OF THE GRANULOCYTE IN THE HEMOLYTIC UREMIC SYNDROME
D.M.W.M. te Loo, V.W.M. van Hinsbergh, T.J.A.M. van der Velden, M. Vermeer, F. Preyers, P. DeMacker, L.P.W.J. van den Heuvel, L.A.H. Monnens (The Netherlands)
P42
D.M.W.M. te Loo, W. Onland, T.J.A.M. van der Velden, L.P.W.J. van den Heuvel, L.A.H. Monnens ( The Netherlands)
P43 TRANSIENT RENAL FUNCTIONAL IMPAIRMENT ASSOCIATED WITH PARENTERAL AMPICILLIN AND AESCIN TREATMENT
J. Gut, A. Kolský, V. Němec, M. Pánek (Czech Republic)
P44 ACUTE RENAL FAILURE IN CHILDREN IN WALES; A PROSPECTIVE EPIDEMIOLOGICAL STUDY
A. Imam, R. Roberts, K. Verrier-Jones (United Kingdom)
P45 IMPAIRED RENAL FUNCTION IN CHILDREN WITH RENAL TUMORS TREATED WITH
E. Kapinga, G. Kardos, J. van der Deure, J.A.E. van Wijk (The Netherlands)
P46 CHRONIC RECURRENT / RELAPSING HUS: CASE REPORT
T. Šuláková, H. Ptoszková, B. Blažek, L. Mrhačová, J. Pták, J. Slaný (Czech Republic)
P47 LONG-TERM OUTLOOK IN CHILDHOOD HAEMOLYTIC-URAEMIC SYNDROME
A. Zurowska, Z. Gockowska, P. Czarniak, E. Marczak (Poland)
P48 NEONATAL END STAGE RENAL FAILURE ASSOCIATED WITH MATERNAL ASSUMPTION OF NIMESULIDE AS TOCOLYTIC
L. Peruzzi, B. Gianoglio, G. Porcellini, O. Sernia, R. Coppo (Italy)
P49 ATYPICAL HEMOLYTIC-UREMIC SYNDROME
A. Peco-Antic, O. Jovanovic, M. Kostic, D. Kruscic (Yugoslavia)
P50 ACUTE RENAL FAILURE (ARF) IN CHILDREN WITH PRIMARY NEPHROTIC SYNDROME
K. Kilis-Pstrusinska, D. Zwolinska, K. Musial (Poland)
P51 HEMOLYTIC UREMIC SYNDROME (HUS) ASSOCIATED WITH ENTEROHEMORRHAGIC ESCHERICHIA COLI
H.M. Verweyen, H. Karch, F. Allerberger, L.B. Zimmerhackl (Germany)
P52 EFFICACY OF PERITONEAL DIALYSIS IN ACUTE RANAL FAILURE IN CHILDREN AFTER CARDIO-PULMONARY BY-PASS SURGERY
J. Slaviček, Z. Puretic, M. Novak, I. Malčic, B. Filipovic, D. Šaric, T. Luetic, S. Batinica, S. Glavaš-Boras, Z. Marekovic (Croatia)
P53 THROMBOTIC THROMBOCYTOPENIC PURPURA IN AN ADOLESCENT WITH CONGENITAL CHRONIC RELAPSING MICROANGIOPATHIC ANEMIA AND THROMBOCYTOPENIA
F. Ringelmann, B. Gruhn, K. Kentouche, L. Patzer, G. Rönnefarth, J. Misselwitz (Germany)
P54 LATE SEQUELS OF CHILDREN WITH HEMOLYTIC-UREMIC SYNDROME (HUS) IN CZECH REPUBLIC
K. Bláhová, J. Janda, J. Kreisinger, E. Matějková, B. Bielaszewska (Czech Republic)

Poster Session 3b)
HYDRONEPHROSIS / BLADDER DYSFUNCTION / ENURESIS

Chairperson: L. Kovács (Slovakia), M. Nuutinen (Finland)

P67 EFFICACY AND SAFETY OF DESMOPRESSIN (ADIURETIN SD) NASAL DROPS IN CHILDREN WITH PRIMARY NOCTURNAL ENURESIS
V. Bačiulis, A. Malikënas, B. Pundzienë, J. Masalskienë, R. Kiudelienë (Lithuania)
P68 ANGIOTENSIN CONVERTING ENZYME GENE POLYMORPHISM AND RENAL DAMAGE IN CHILDHOOD UROLOGICAL DISEASES
A. Al-Eisa, M.Z. Haidar, B.S. Srivasta (Kuwait)
P69 RESULTS IN MANAGEMENT OF PATIENTS WITH ANTENATALLY DIAGNOSED PELVI-URETERIC FUNCTION OBSTRUCTION
U. John, P. Seidel, S. Vogt, M. Beintker, C. Luck, J. Misselwitz (Germany)
P70 SERUM LEVELS OF ANGIOTENSIN CONVERTING ENZYME IN INFANTS WITH
P. Geier, M. Budíková, H. Flögelová (Czech Republic)
P71 HYDRONEPHROSIS ON ANTENATAL ULTRASOUND: POSTNATAL OUTCOME
H. Kapadia, K.-J. Lidefelt, U. Erasmie, C. Pilo (Sweden)
P72 BLADDER-DYSFUNCTION IS THE MAJOR CAUSE OF FIRST UTI IN CHILDREN >2,5 Y
A. Raes, A. France, S. Van Aken, P. Hoebeke, E. Van Laecke, J. Vande Walle (Belgium)
P73 NOCTURNAL POLYURIA IN ENURETICS IS RELATED TO ABNORMALITIES, NOT ONLY OF DAY-NIGHT RYTHM OF DIURESIS, BUT OF RENAL FUNCTION AND SALTHANDLING
J. Thijs, A. Raes, E. Van Laecke, P. Hoebeke, J. Vande Walle (Belgium)
P74 MAGNETIC RESONANCE IN PEDIATRIC NEPHRO-UROLOGY
M. Hall, F. Avni, K. Ismaili, N. Nicaise, T. Schurmans, F. Janssen, F. Collier (Belgium)
P75 POSTNATAL VERSUS ANTENATAL ULTRASOUND SCREENING FOR URINARY TRACT ABNORMALITIES
L. Cataldi, R. Galiano, S. Sani, V. Fanos, R. Agostiniani (Italy)
P76 CLINICAL AND RADIOLOGICAL OUTCOME OF UNILATERAL MULTICYSTIC DYSPLASTIC KIDNEY (MCDK)
S. Sukthankar, A.R. Watson (UK)
P77 ANGIOTENSIN I CONVERTING ENZYME (ACE) GENE INSERTION/DELETION (I/D) POLYMORPHISM IN CHILDREN WITH FUNCTIONAL INCONTINENCE
A. Stankovic, M. Kostic, A. Peco-Antic, D. Alavantic, S. Glisic, N. Ilic, O. Jovanovic, D. Kruscic (Yugoslavia)
P78 ANGIOTENSIN I-CONVERTING ENZIME (ACE) GENE INSERTION/DELETION (I/D) POLYMORPHISM IN CHILDREN WITH PRIMARY NIGHTTIME-BED WETTING
M. Kostic, A. Stankovic, D. Alavantic, A. Peco-Antic, S. Glisic, O. Jovanovic, N. Ilic, D. Kruscic (Yugoslavia)
P79 CHILDREN WITH BLADDER DYSFUNCTION: CLINICAL CHARACTERIZATION OF PATIENTS AND RESULTS OF BLADDER TRANING
E. Gäbel, Ch. Heiken-Löwenau, M. Bald, K.E. Bonzel (Germany)
P80 SYMPATHETIC SKIN RESPONSE IN CHILDREN WITH ENURESIS
V.G. Maidannik, I.A. Miyiuriaeva, N.V. Molochek, I.A. Afanasjeva (Ukraine)

Poster Session 4b)
ARTERIAL HYPERTENSION

Chairperson: J.L. André (France), M. Dillon (United Kingdom)

P93 ANGIOTENSIN-CONVERTING ENZYME GENE POLYMORPHISM AS CARDIOVASCULAR RISK FACTOR IN CHILDREN
N. Marčun-Varda, B. Peterlin, S. Umek Bradač, A. Gregorič, T. Milanez (Slovenia)
P94 THE DISTRIBUTION OF RENIN-CONTAINING CELLS IN MULTICYSTIC DYSPLASTIC KIDNEYS
R. Konda, K. Sakai, S. Otal, T. Hatakeyama, Y. Abel, S. Orikasa, N. Kimura (Japan)
P95 COUGH IS COMMON IN CHILDREN PRESCRIBED CONVERTING ENZYME INHIBITORS
R.O. von Vigier, A.C. Truttmann, M.G. Bianchetti (Switzerland)
P96 ARTERIAL HYPERTENSION IN SCHOOL CHILDREN: FREQUENCY AND GENETIC FACTORS
M. Pavicevic, D. Pavicevic, B. Ugrinovic, S. Obradovic, G. Kostic, D. Madzarac (Yugoslavia)
P97 COMPARISON OF TWO DIFFERENT METHODS FOR BLOOD PRESSURE MEASUREMENT IN CHILDREN WITH POLYCYSTIC KIDNEY DISEASE
V. Lehotská, T. Kernová, V. Hupka, Z. Shah, A. Šufliarská (Slovakia)
P98 ELEVATED SODIUM AND NITRATE LEVELS IN THE DRINKING WATER CONTRIBUTE TO THE ELEVATION OF BLOOD PRESSURE LEVELS IN SCHOOL CHILDREN
A. Pomeranz, Z. Korzets, D. Vanunu, T. Dolfin, B. Wolach (Israel)
P99 PERCUTANEOUS TRANSLUMINAL ANGIOPLASTY FOR RENOVASCULAR HYPERTENSION
R. Davies, M. Barkovics, I. Gordon, V. Shah, M. Chan, M. Dillon (UK)
P100 EVALUATION OF THE TREATMENT RESULTS IN 58 CHILDREN WITH RENOVASCULAR
A. Wieteska-Klimczak, E. Cichocka, J. Antoniewicz, T. Wyszynska, P. Januszewicz (Poland)
P101 PLASMA ENDOTHELIN, PLATELET AGGREGATION AND THROMBOXANE RELEASE IN PROGRESSIVE RENAL DISEASES AND IN ESSENTIAL HYPERTENSION
F. Papp, É. Sallay, C. Bereczki, I. Haszon, S. Túri (Hungary)
P102 THE ROLE OF OXIDATIVE STRESS IN THE PATHOGENESIS OF JUVENILE ESSENTIAL AND RENAL HYPERTENSION
C. Bereczki, I. Varga, F. Papp, I. Haszon, B. Matkovicz, S. Túri (Hungary)
P103 TWENTY-FOUR-HOUR AMBULATORY BLOOD PRESSURE MONITORING IN HEALTHY
A. Borowski, A. Wieteska-Kimczak, T. Dorywalski, T. Wyszynska, P. Januszewicz (Poland)
P104 CHANGES IN LEFT VENTRICULAR MASS AND 24-HOUR SYSTOLIC BLOOD PRESSURE
M.C. Matteucci, U. Giordano, A. Calzolari, A. Santilli, G. Rizzoni (Italy)
P105 THE CLINICAL SIGNIFACANCE OF HYPERTENSION (HT) IN CHILDREN WITH GLOMERULONEPHRITIS (GN)
V.P. Sitnikova, T.L. Nastausheva, L.I. Stakhourlova, V.N. Penkin, E.L. Panchenko (Russia)
P106 INDICATION AND STANDARD OF HOME BLOOD PRESSURE MEASUREMENT IN CHILDREN AND ADOLESCENTS: SURVEY AMONG GERMAN PAEDIATRIC NEPHROLOGISTS
M. Bald, P.F. Hoyer (Germany)
P107 ESSENTIAL HYPERTENSION IN CHILDREN AND ADOLESCENTS: FIRST CLINICAL DATA FROM 22 PATIENTS EVALUTED BY AMBULATORY BLOOD PRESSURE MONITORING
R. Büscher, K.J. Eilmes, M. Bald, P.F. Hoyer (Germany)

Poster Session 5b)
NEPHROTIC SYNDROME

Chairperson: A. Bensman (France),

P123 SEVERE HEMORRHAGE DUE TO PARVOVIRUS B 19 INFECTION IN AN IMMUNOCOMPROMISED GIRL WITH IGA NEPHRITIS
J. Dušek, K. Vondrák, T. Seeman, J. Feber, J. Janda, I. Hadačová (Czech Republic)
P124 NEPHROTIC SYNDROME IN A CHILD WITH CHRONIC GRANULOMATOUS DISEASE (CGD) AND INVASIVE ASPERGILLOSIS
P. Kaltenis, S. Maknavičius (Lithuania)
P125 IMMUNE STATUS OF CHILDREN SUFFERING FROM IDIOPATHIC NEPHROTIC SYNDROME
N.N. Sang, L.N. Tra, P.T.P. Phi (Vietnam)
P126 BUDD-CHIARI SYNDROME AND INFERIOR VENA CAVA THROMBOSIS IN A CHILD WITH NEPHROTIC SYNDROME
M. Lilova, I. Velkovski, N. Velichkov (Bulgaria)
P127 HLA ANTIGENS IN NEPHROTIC SYNDROME
A. Noyan, A. Karabay Bayazit, Y. Bayazit, A. Anarat (Turkey)
P128 LOW SERUM HOMOCYSTEINE LEVELS IN CHILDHOOD NEPHROTIC SYNDROME
S. Feinstein, B.A. Sela, D. Raveh, R. Becker-Cohen, Y. Frishberg (Israel)
P129 IMMUNE RESPONSE DISORDERS IN DIFFERENT STAGES OF IDIOPATHIC NEPHROTIC SYNDROME AND TREATMENT OPTIONS FOR THE PREVENTION OF RELAPSE
J. Liška, E. Horáková, I. Ulčová, V. Zavázal, A. Stajner, V. Kraus, V. Gutová (Czech Republic)
P130 NEPHROTIC SYNDROME AFTER CONTACT DERMATITIS BY ACUTE SKIN EXPOSURE TO TAR DERIVATES
E. Urdaneta-Carruyo, A. Suranyi, I. Hernandez, L.M. Guilarte (Hungary)
P131 PNEUMOCOCCAL POLYSACCHARIDE IMMUNIZATION IN CHILDREN WITH NEPHROTIC SYNDROME
E. Bahat, M. Senyurt, S. Akman, A. Gür Güven (Turkey)
P132 PATTERN OF NEPHROTIC SYNDROME IN EAST NORTH PART OF EGYPT IN THE LAST 5 YEARS
A.A. Sarhan, A.M. Bakr, A.M. Hammad, M.R. Yousef (Egypt)
P133 STUDY OF INTERLEUKIN-8 IN CHILDREN WITH PRIMARY EPHROTIC SYNDROME
A.A. Sarhan, A.M. Bakr, F. El-Shenawy, M.A. Shokeir, A.M. Hammad, M.R. Yousef, W.A. Seleim (Egypt)
P134 NITRIC OXIDE AND CHRONIC GLOMERULONEPHRITIS IN CHILDREN
A. Kucherenko, Ch. Markov, D. Matkerimov, T. Sergeeva (Russia)
P135 PURTSCHER´S RETINOPATHY IN A 4-YEAR OLD BOY WITH NEPHROTIC SYNDROME AND CHRONIC RENAL FAILURE- A CASE REPORT
D. Zwolinska, A. Medynska, A. Galar, A. Turno (Poland)
P136 CLINICAL PRESENTATION AND TREATMENT OF THROMBOEMBOLISM IN CHILDREN WITH KIDNEY DISEASES
T. Jarmolinski, J. Maciejewski (Poland)
P137 NEPHROTIC SYNDROME OF CHILDHOOD
H. Alpay, A. Canbolat, K. Babaoglu, N. Yildiz, Y. Kozok, S. Özcay (Turkey)
P138 Th1 CYTOKINES, IL12 AND IFN? IN CHILDHOOD IDIOPATHIC NEPHROTIC SYNDROME
E. Golubovic, P. Miljkovic, V. Stefanovic, M. Zlatkovic, S. Živic, P. Vlahovic (Yugoslavia)
P139 EXAMINATION OF NITRIC OXIDE ACTIVITY IN CHILDREN WITH NEPHROTIC SYNDROME (NS)
A.V. Malkoch, E.G. Kurbanova, M.S. Ignatova, V.A. Tabolin (Russia)
P140 SERUM CARNITINE IN CHILDREN WITH NEPHROTIC SYNDROME
H. Mocan, A. Aksoy, T. Camlibel (Turkey)
P141 UNUSUAL ASSOCIATION OF GLOMERULONEPHRITIS AND HODGKIN LYMPHOMA
B. Ranchin, R. Bouvier, L. Dubourg, M. Chambon, N. Philippe, P. Cochat (France)
P142 DOWN REGULATION OF IKBA IN MINIMAL CHANGE DISEASE (MCD)
A. Bensman, P. Lang, P. Remy, D. Sahali (France)

Poster Session 6b)
VASCULITIS AND SYSTEMIC DISEASES

Chairperson: J.C. Davin (The Netherlands), F. Perfumo (Italy)

P158 A FAMILY WITH HYPERIMMUNOGLOBULIN M SYNDROME AND SYSTEMIC AMYLOIDOSIS
A.Öner, G. Demircin, Ö. Erdgan, M. Bülbül, L. Memis, K. Tinaztepe, I. Aksentijevich (Turkey)
P159 THE EFFECT OF QUADRUPLE THERAPY IN CHILDHOOD LUPUS NEPHRITIS
A. Öner, G. Demircin, M. Bülbül, Ö. Erdogan, A. Poyraz, L. Memis, K. Tinaztepe (Turkey)
P160 LACK OF EFFICACY OF VITAMIN E SUPPLEMENTATION IN DECREASING THE OXIDATIVE DAMAGE IN HENOCH-SCHÖNLEIN PURPURA: A RANDOMISED CONTROLLED TRIAL
Ö. Erdogan, A. Öner, A. Aydin, A. Isimer, G. Demircin, M. Bülbül, A. Sahin (Turkey)
P161 VASCULAR ENDOTHELIAL GROWTH FACTOR IN HENOCH SCHOENLEIN PURPURA
R. Topaloglu, U. Saatci, A. Bakkaloglu, E. Baskn, N. Besbas (Turkey)
P162 THE ROLE OF NITRIC OXIDE (NO), TUMOR NECROSIS FACTOR (TNF) ? AND INTERLEUKIN (IL) - 1ß IN HENOCH-SCHÖNLEIN VASCULITIS IN CHILDHOOD
N. Buyan, O. Söylemezoglu, N. Akkök, D. Erbas, E. Hasanoglu (Turkey)
P163 NEPHROTIC SYNDROME IN PATIENTS WITH JUVENILE CHRONIC ARTHRITIS
A. Jankauskiene, P. Kaltenis, V. Panaviene, A. Malikenas, A. Garkauskiene (Lithuania)
P164 LONG-TERM FOLLOW-UP OF ANTINEUTROPHIL CYTOPLASMIC AUTOANTIBODIES (ANCA)-POSITIVE GLOMERULONEPHRITIS (GN) AND VASCULITIS IN CHILDREN
G. Barbano, M.L. Degl´Innocenti, R. Gusmano, F. Perfumo (Italy)
P165 THE EFFECT OF PROPHYLACTIC PREDNISOLON THERAPHY ON RENAL INVOLVEMENT IN HENOCH SCHÖNLEIN VASCULITIS
I. Islek, T. Sezer, M. Totan, M. Cakir, S. Kücüködük (Turkey)
P166 CLINICAL, LABORATORY AND MOLECULAR CHARACTERISTICS OF CHILDREN WITH
M. Tekin, F. Yalcinkaya, N. Tümer, N. Akar, M. Misirhoglu, N. Cakar, H. Tastan, H. Kocak (Turkey)
P167 CEREBRAL VASCULITIS IN HENOCH-SCHÖNLEIN PURPURA
S.A. Bakkaloglu, M. Ekim, N. Tümer, G. Deda, I. Erdem, T. Erdem (Turkey)
P168 THE COURSE OF END STAGE RENAL FAILURE (ESRF) DUE TO SECONDARY AMYLOIDOSIS (A) AND GLOMERULONEPHRITIS (GN)
B. Wojciechowska, M. Roszkowska-Blaim, M. Sieniawska (Poland)
P169 TUBULAR FUNCTIONS IN FAMILIAL MEDITERRANEAN FEVER
S. Akkus, S. Caliskan, Ö. Kasapcopur, L. Sever, E. Akdenizli, I. Bilge, N. Arisoy (Turkey)
P170 LUPUS NEPHRITIS IN CHILDREN: PROGNOSTIC SIGNIFICANCE OF CLINICO-PATHOLOGICAL FINDINGS AND THERAPEUTIC APPROACHES
S. Emre, I. Bilge, A. Nayir, A. Sirin, I. Kilicaslan, V. Uysal (Turkey)

Poster Session 7b)
GROWTH IN CRF: PATHOPHYSIOLOGY AND TREATMENT

Chairperson: C. Chantler (United Kingdom), F. Santos (Spain)

P186 SERUM IGFBP-4 AND -5 LEVELS IN CHILDREN WITH CHRONIC RENAL FAILURE (CRF): RELATIONSHIP TO GROWTH AND GFR
T. Ulinski, D. Kiepe, S. Mohan, W.F. Blum, A.-M. Wingen, O. Mehls, B. Tönshoff (USA)
P187 DIFFERENTIAL EFFECTS OF INSULIN-LIKE GROWTH FACTOR-BINDING PROTEINS (IGFBPS) ON IGF ACTIVITY IN GROWTH PLATE CHONDROCYTES
T. Ulinski, D.R. Powell, T. Seck, J. Pfeilschifter, O. Mehls, B. Tönshoff (USA)
P188 PLASMA LEVELS OF SOLUBLE CD30 ARE INCREASED IN CHILDREN WITH CHRONIC RENAL FAILURE AND WITH PRIMARY GH DEFICIENCY AND DECREASED DURING TREATMENT WITH RECOMBINANT GH
G. Barbano, F. Cappa, I. Prigione, V. Pistoia, A. Cohen, R. Gusmano, F. Perfumo (Italy)
P189 CHRONIC RENAL FAILURE IN INFANTS: OUTCOME AND GROWTH
J.A. Kari, C.M. Gonzalez Celedon, S.A. Ledermann, V. Shaw, L. Rees (UK)
P190 RISE IN SERUM PROCOLLAGENS DURING GROWTH HORMONE TREATMENT OF
M. Davidovits, L.T. Jensen, A. Silbergeld, B. Klinger, R. Eshet, B. Eisenstein, Z. Laron (Israel)
P191 PTH LEVELS AND PUBERTY IN CHILDREN WITH CHRONIC RENAL FAILURE (CRF)
S. Picca, M. Cappa, C. Martinez, G. Raguso, G. Ardissino, F. Perfumo, R. Bonaudo, G. Montini, S.I. Moges, J. Osborn (Italy)
P192 EFFECT OF EXPERIMENTAL UREMIA ON EXPRESSION OF TYPE X AND TYPE II COLLAGENS IN THE GROWTH PLATE OF UREMIC RATS
J. Álvarez, M. Balbín, F. Santos, M. Fernández, S. Ferrando, A. Weruaga, J.M. López (Spain)
P193 PITUITARY GHRH RECEPTOR GENE EXPRESSION IS NOT MODIFIED BY UREMIA OR MALNUTRITION IN YOUNG RATS
S. Ferrando, J. Rodríguez, F. Santos, A. Weruaga, M. Fernández, J. Álvarez, J.M. López, E. Carbajo (Spain)
P194 BODY COMPOSITION IN CHILDREN WITH CHRONIC RENAL FAILURE (CRF) DURING GROWTH HORMONE TREATMENT
M. Tomaszewska, A. Jedrzejowski, M. Lech, A. Majcher, J. Przedlacki, M. Szczepanska, G. Siten, A. Zurowska, J. Rubik, P. Dyras, J. Stachowski, A. Kaluzynska, M. Sieniawska, M. Roszkowska-Blaim (Poland)
P195 FINAL HEIGHT IN CHILDREN WITH CHRONIC RENAL FAILURE (CRF) ON LONG-TERM GROWTH HORMONE (GH) TREATMENT
R. Nissel, D. Haffner, E. Wühl, F. Schaefer, O. Mehls and the German Study Group for Growth Hormone Treatment in Chronic Renal Failure (Germany)
P196 A NEW CONDITIONALLY IMMORTALIZED CELL-LINE OF GROWTH-PLATE CHONDROCYTES WITHOUT LOSS OF CELL-DIFFERENTIATION
R. Himmele, G. Laitenberger, T. Ulinski, J. Reiser, P. Mundel, O. Mehls (Germany)
P197 DIFFERENTIATION OF GROWTH PLATE CHONDROCYTES INTO CELLS WITH OSTEOBLAST-LIKE PROPERTIES
R. Himmele, G. Laitenberger, T. Ulinski, G. Klaus, B. Tönshoff, O. Mehls (Germany)
P198 UREMIC SERUM FRACTIONS INHIBIT SECRETION OF GONADOTROPIN-RELEASING HORMONE FROM GT 1-7 NEURONS
M. Daschner, T. Nguyen, R. Wiesner, O. Mehls, F. Schaefer (Germany)
P199 LONG-TERM EFFECTS OF TUBE FEEDING ON GROWTH AND BODY COMPOSITION IN UREMIC INFANTS
R. Feneberg, E. Bürkel, K. Sahm, K. Weck, O. Mehls, F. Schaefer (Germany)
P200 LONG-TERM RESULTS OF GROWTH HORMONE TREATMENT IN CHILDREN WITH NEPHROPATHIC CYSTINOSIS
E. Wühl, D. Haffner, G. Offner, M. Broyer, W. van´t Hoff, O. Mehls (Germany)

Poster Session 8b)
PERITONEAL DIALYSIS

Chairperson: R. Donckerwolcke (Canada), M. Bulla (Germany)

P215 IMPROVED CPD OUTCOME IN SMALL CHILDREN UNDER ADEQUACY CONTROL
T. Hölttä, K. Rönnholm, M. Antikainen, C. Holmberg (Finland)
P216 HOSPITALISATION RATE IN PERITONEAL DIALYSIS AND HEMODIALYSIS PATIENTS - ONE CENTRE ANALYSIS
A. Czupryniak, A. Kaluzynska, M. Tkaczyk, A. Jander, D. Finke (Poland)
P217 ACUTE PANCREATITIS IN CHILDREN WITH PERITONEAL DIALYSIS ASSOCIATED WITH ANGIOTENSIN CONVERTING ENZYME INHIBITORS
B. Enke, T. Henne, G. Offner, J.H.H. Ehrich (Germany)
P218 PATIENT AND TECHNIQUE SURVIVAL IN PEDIATRIC PATIENTS ON CHRONIC PERITONEAL DIALYSIS (CPD) AND HEMODIALYSIS (HD). A 9-YEAR MULTICENTER EXPERIENCE
E. Verrina, F. Perfumo, A. Edefonti, P. Sorino, S. Rinaldi, B. Gianoglio, G. Zacchello (Italy)
P219 BIOIMPEDANCE (BIA) SUGGESTS PRESENCE OF FLUID SHIFT BETWEEN EXTRA- AND INTRACELLULAR WATER DURING HD
L. Pátri, A. Karátson, Z. Németh, E. Sulyok (Hungary)
P220 KINETICS OF FORMATION OF GLYCATION PRODUCTS IN PERITONEAL DIALYSIS: COMPARISON BETWEEN ICODEXTRIN AND GLUCOSE SOLUTIONS
A. Amore, P. Cirina, G. Conti, P. Belardi, F. Giacchino, R. Coppo (Italy)
P221 VALUE OF HIGH RESOLUTION ULTRASONOGRAPHY IN MONITORING PERITONEAL
J. Vande Walle, J. Verbanck, I. Vande Wiele, A. Raes, P. Hansen, M. Segaert (Belgium)
P222 AUTOMATED PERITONEAL DIALYSIS (APD) DATA SCANNING BY TELEDIALYSIS
A. Edefonti, S. Boccola, B. Damiani, M. Picca, C. Maroli, G. Marra, M. Giani, G. Ardissino, L. Ghio, M.T. Parisotto, C. Cerrato (Italy)
P223 HERNIA DEVELOPMENT IN CHILDREN WITH CAPD
N. Özkaya, N. Tümer, F. Yalcinkaya, M. Ekim (Turkey)
P224 MIDDLE MOLECULES AND SMALL PREOTEINS CLEARANCE IN CHILDREN ON PERITONEAL DIALYSIS
G. Montini, G. Amici, L. Murer, S. Milan, B. Andreetta, R. Dall´Amico, I. Tätch, A. Ammenti, M. Mussap, M. Natural, G. Zacchello (Italy)
P225 EVALUATION OF RESIDUAL PERITONEAL VOLUME IN CHILDREN ON PERITONEAL DIALYSIS
C.P. Schmitt, R. Dötschmann, M. Daschner, M. Zimmering, C. Greiner, M. Böswald, G. Klaus, O. Mehls, F. Schaefer (Germany)
P226 BLOOD PRESSURE AND WATER COMPARTMENTS ESTIMATED BY BIOELECTRICAL IMPEDANCE (BIA) IN DIALYZED CHILDREN
D. Drozdz, P. Dyras, K. Sancewicz-Pach, J.A. Pietrzyk, K. Zachwieja (Poland)
P227 COMPLICATIONS OF CAPD/CCPD IN CHILDREN - A MULTICENTRIC STUDY
S. Caliskan, A. Sirin, H. Alpay, S. Emre, L. Sever, Y. Kozok, N. Yildiz, F. Öktem, P. Turhan, I. Bilge, N. Arisoy, A. Nayir, C. Kosan, and Istanbul Pediatric Nephrology Working Group (Turkey)
P228 ORAL VITAMIN INTAKE IN CHILDREN RECEIVING LONG-TERM DIALYSIS
A.M. Pereira, N. Hamani, P. Koch Nogueira, J.T.A. Carvalhaes (Brazil)

Poster Session 9b)
ORGAN TRANSPLANTATION

Chairperson: F. Janssen (Belgium), J. Ehrich (Germany)

P242 ORGAN ALLOCATION IN PEDIATRIC TRANSPLANTATION IN FRANCE
C. Loirat, Y. Chalem, J.L. Golmard (France)
P243 IMPROVEMENT OF CYSTINOSIS ENCEPHALOPATHY BY CYSTEAMINE TREATMENT (CASE REPORT)
M. Wigger, E. Drückler, J. Muscheites, B.W. Cornelißen, R. Terpe, H.J. Stolpe (Germany)
P244 DE NOVO CANCERS IN PEDIATRIC RENAL TRANSPLANT RECIPIENT: A MULTICENTER ANALYSIS WITHIN NORTH ITALY TRANSPLANT PROGRAM (NITp)
A. Nocera, I. Fontana, L. Ghio, R. Dall´Amico, M. Cardillo, F. Ginevri (Italy)
P245 RENAL FUNCTION IN CHILDREN BEFORE AND AFTER LIVER TRANSPLANTATION
U. Berg, A. Nemeth (Sweden)
P246 MODULATION OF NITRIC OXIDE SYNTHASE ACTIVITY AND APOPTOSIS IN ENDOTHELIAL CELLS: COMPARISON BETWEEN CYCLOSPORIN (CyA), FK506 AND MOFETIL MYCOPHENOLATE (MMF)
G. Conti, A. Amore, P. Cirina, R. Coppo (Italy)
P247 CHARACTERISATION OF CYCLOSPORIN (CsA) RESISTANT ALLO-SPECIFIC CYTOTOXIC CELLS IN NEONATAL BLOOD
C. Truman, K. Haque, J. Dudley, J.M. Hows, B.A. Bradley (UK)
P248 WHICH T-CELL RELATED GENES ARE ACTIVATED IN PRIMARY AND RECURRENT FOCAL SEGMENTAL SCLEROSIS (FSGS)?
J. Strehlau, C.v. Schnakenburg, A.D. Schachter, A. Strasburg, G. Offner, K. Latta, B. Enke, G. Filler, B. Klare, A. Tejani, T.B. Strom, J.H.H. Ehrich (Germany)
P249 INFECTIONS IN PEDIATRIC KIDNEY AND LIVER TRANSPLANT PATIENTS
M. Their, C. Holmberg, I. Lautenschlager, K. Höckerstedt, H. Jalanko (Finland)
P250 DURATION OF INTERLEUKIN-2 RECEPTOR (IL-2R) SATURATION BY BASILIXIMAB IN PEDIATRIC RENAL TRANSPLANT RECIPIENTS
V. Baudouin, G. Sterkers, H. Ansart, P. Niaudet, P. Cochat, C. Loirat (France)
P251 NEPRHOTOXICITY OF TACROLIMUS (TAC) AND CYCLOSPORINE A (CYA): AN IN VITRO MODEL
N. Gordjani, T. Epting, P.F. Riepe, R. Nitschke, R. Greger, M. Brandis (Germany)
P252 INCIDENCE OF CYTOMEGALOVIRUS (CMV) INFECTIONS IN PEDIATRIC RENAL TRANSPLANT RECIPIENTS
L.T. Weber, I. Giurgea, J.J. Bugert, O. Mehls, B. Tönshoff (Germany)
P253 GANCICLOVIR RESISTANT CMV DISEASE IN A PEDIATRIC RENAL TRANSPLANT RECIPIENT
L.T. Weber, J.J. Bugert, C.P. Schmitt, O. Mehls, B. Tönshoff (Germany)
P254 CHARACTERIZATION OF THE GENES UPREGULATED IN THE MINIMAL CHANGE DISEASE (MCD) AND RECURRENT POST TRANSPLANT NEPHROSIS
D. Sahali, A. Pawlak, P. Lang, P. Remy, A. Bensman, G. Guellaen (France)
P255 CONVERSION FROM AZATHIOPRINE TO MYCOPHENOLATE MOFETIL IN PEDIATRIC RENAL TRANSPLANT RECIPIENTS
M. Charbit, G. Guest, M.F. Gagnadoux, P. Niaudet, M. Broyer (France)

13.15 - 14.45 Symposium S7 AUDITORIUM 1
NOVEL ASPECTS ON THE REGULATION OF WATER METABOLISM
Chairperson: A. Aperia (Sweden), T. Tulussay (Hungary)

• ROLE OF WATER CHANNELS FOR THE ADAPTATION TO POSTNATAL LIFE - M. Yasui (USA)
• BIDIRECTIONAL REGULATION OF WATER TRANSPORT BY AVP AND PROSTAGLANDIN E2 - M. Zelenina (Sweden)
• MOLECULAR MECHANISM OF DECREASED URINARY CONCENTRATING CAPACITY IN OBSTRUCTIVE NEPHROPATHY - F. Frökiaer (Denmark)


13.15 - 14.45 Symposium S8 AUDITORIUM 2
GROWTH DISTURBANCE IN CHRONIC RENAL FAILURE
Chairperson: F. Santos (Spain), B. Tönshoff (Germany)
Sponzored by Pharmacia & Upjohn

• MECHANISM CONTROLLING CHONDROCYTE DIFFERENTIATION - R. Cancceda (Italy)
• RhGH TREATMENT OF UREMIC GROWTH FAILURE - LONG-TERM RESULTS AND FUTURE ASPECTS - R.N. Fine (USA)
• HIGH DOSE GROWTH HORMONE TREATMENT IN SHORT STATURE AFTER INTRAUTERINE GROWTH RETARDATION AND IN GLUCOCORTICOID-INDUCED GROWTH FAILURE - P. Czernichow (France)


14.45 - 16.15 Free Communications III. AUDITORIUM 1
CHRONIC RENAL FAILURE AND DIALYSIS
Chairperson: V. Teplan (Czech Republic), E.Verrina (Italy)
14.45 - 14.58
O11 CHANGES OF AUTONOMIC CARDIOVASCULAR REGULATION MEASURED BY SPECTRAL ANALYSES OF BLOOD PRESSURE IN CHILDREN AND ADOLESCENTS WITH CHRONIC RENAL FAILURE
M. Bald, H. Rüdiger, H. Senkabak, D. Sahin, K.E. Bonzel, P.F. Hoyer (Germany)
14.58 - 15.11
O12 PRE-TRANSPLANT THROMBOPHILIA SCREENING IN CHILDREN WITH CHRONIC RENAL FAILURE (CRF)
J. Oh, A. Veldmann, W. Kreuz, I. Scharrer, O. Mehls, F. Schaefer (Germany)
15.11 - 15.24
O13 BRAIN ADAPTATION TO WATER LOADING IN RABBITS AS ASSESSED BY NMR RELAXOMETRY
E. Berényi, Z. Vajda, P. Bogner, I. Repa, T. Dóczi, E. Sulyok (Hungary)
15.24 - 15.37
O14 ICODEXTRIN STUDIES IN CHILDREN ON PD
A.W. de Boer, C.H. Schröder, J.L. Willems, L.A.H. Monnens (The Netherlands)
15.37 - 15.50
O15 GLYCATED PRODUCTS INDUCED BY PERITONEAL DIALYSIS SOLUTION TURN-ON FIBROBLAST-LIKE TRANSDIFFERENTIATION IN MESOTHELIAL CELLS: COMPARISON BETWEEN ICODEXTRIN AND GLUCOSE
A. Amore, G. Conti, P. Cirina, R. Coppo (Italy)
15.50 - 16.15
** Invited Lecture ** EDTA-REPORT: THE SIGNIFICANCE OF RECURRENT RENAL DISEASES FOR TRANSPLANT SURVIVAL
O. Mehls (Germany), S. Rigden (UK)

14.45 - 16.15 Free Communications IV. AUDITORIUM 2
GENE POLYMORPHISM: SIGNIFICANCE FOR UROPATHY, PROGRESSION OF CRF AND TRANSPLANT SURVIVAL
Chairperson: G.M. Ghiggeri (Italy), L. Kovács (Slovakia)
14.45 - 15.10
** Invited Lecture ** CYTOKINE GENE POLYMORPHISM: A PREDICTOR OF RENAL TRANSPLANT SURVIVAL
I.V. Hutchinson (United Kingdom)
15.10 - 15.23
O16 IS PUBERTY A RISK FACTOR FOR PROGRESSION OF CHRONIC RENAL INSUFFICIENCY (CRI)?RELAXOMETRY
G. Ardissino, V. Dacco, A. Claris-Appiani, S. Testa, S. Loi , F. Sereni (Italy)
15.23 - 15.36
O17 ACE I/D GENOTYPE IS ASSOCIATED WITH SCAR FORMATION IN CHILDREN WITH VESICOURETERAL REFLUX
L. Kovács, J. Gut, T. Šuláková, O. Hamidová, A. Šufliarska (Slovakia)
15.36 - 15.49
O18 INFLUENCE OF ANGIOTENSIN CONVERTING ENZYME (ACE) I/D GENE POLYMORPHISM ON PARENCHYMAL LESIONS IN CONGENITAL UROPATHIES
K. Hohenfellner, P. Brodhag, R. Brezinska, W. Mannhardt, V. Kon (Germany - USA)
15.49 - 16.02
O19 LOCAL HYPERACTIVITY OF ANGIOTENSIN CONVERTING ENZYME (ACE) IN KIDNEYS OF IgA NEPHROPATHY PATIENTS: RELATIONSHIP WITH ACE GENOTYPE AND PROGRESSION TO RENAL FAILURE
R. Coppo, A. Amore, D. Roccatello, M. Alpa, B. Gianoglio, L. Bertola, G. Mazzola, G. Picciotto (Italy)
16.02 - 16.15
O20 GENETIC VARIANTS OF THE RENIN-ANGIOTENSIN SYSTEM (RAS) AND KIDNEY GRAFT LONG-TERM OUTCOME IN PEDIATRIC RECIPIENTS
F. Perfumo, Pediatric Kidney Transplantation Study Group of the North Italy Transplant program (NITp) Genoa, Milan, Padua (Italy)

16.15 - 16.30 Coffee Break

16.30 - 17.10 State of the Art Lecture L4 AUDITORIUM 1
PATHOGENESIS AND TREATMENT OF PRIMARY GLOMERULONEPHRITIS
K. Matoušovic (Czech Republic)

17.15 - 18.15 ESPN General Assembly AUDITORIUM 2

20.30 - 24.00 Annual Dinner AUDITORIUM 1